N-sulfoglucosamine sulfohydrolase

Preferred Label : N-sulfoglucosamine sulfohydrolase;

MeSH note : believed to be defect in mucopolysaccharidosis IIIA (Sanfilippo syndrome A);

CISMeF synonym : heparin N-sulfatase;

MeSH synonym : sulfoglucosamine sulfamidase; sulfamate sulfohydrolase; sulfamate sulfatase; sulfamidase; sulphamate sulphamidase; sulphamidase; sulphoglucosamine sulphamidase; 2-deoxy-D-glucoside-2-sulfamate sulfohydrolase;

MeSH hyponym : N-sulfoglucosamine sulfohydrolase (sulfamidase) protein, mouse; heparin sulfamidase; heparin sulfamatase; N-sulfoglucosamine sulfohydrolase protein, human; SFMD protein, human; MPS3A protein, human;

MeSH Related Number : SGSH protein, human; sgsh protein, mouse; EC 3.10.1.1;

Registry Number MeSH : EC 3.10.1.1;

Related CAS MeSH : EC 3.10.1.1 (Sgsh protein, mouse); EC 3.10.1.1 (SGSH protein, human);

related registry number list (CISMeF) : EC 3.10.1.1;

Is substance : O;

UNII : EC 3.10.1.1;

Details

Origin ID

C022708;

UMLS CUI

C0075625;

MeSH indexing information
- mucopolysaccharidosis iii [MeSH Descriptor]
MeSH term(s) associated for indexing
- hydrolases [MeSH Descriptor]
Record concept(s)
- N-sulfoglucosamine sulfohydrolase [MeSH concept]
- SGSH protein, human [MeSH concept]
- heparin N-sulfatase [MeSH concept]
- sgsh protein, mouse [MeSH concept]
Semantic type(s)
- Amino Acid, Peptide, or Protein [UMLS semantic type]
- Enzyme [UMLS semantic type]
UMLS correspondences (same concept)
- N-Sulfoglucosamine sulfohydrolase (substance) [SNOMED CT concept]
- n-sulfoglucosamine sulfohydrolase [SNOMED Notion]

Keyword's position in hierarchy(ies) :

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