" /> 1-pyrroline-5-carboxylate dehydrogenase - CISMeF





Preferred Label : 1-pyrroline-5-carboxylate dehydrogenase;

MeSH definition : An enzyme that catalyzes the oxidation of 1-pyrroline-5-carboxylate to L-GLUTAMATE in the presence of NAD. Defects in the enzyme are the cause of hyperprolinemia II.;

MeSH synonym : dehydrogenase, ggs; dehydrogenase, glutamic-gamma-semialdehyde; dehydrogenase, glutamyl-gamma-semialdehyde; dehydrogenase, 1-pyrroline-5-carboxylate; delta(1)-pyrroline-5-carboxylate dehydrogenase; ggs dehydrogenase; glutamic gamma semialdehyde dehydrogenase; glutamic-gamma-semialdehyde dehydrogenase; glutamyl gamma semialdehyde dehydrogenase; glutamyl-gamma-semialdehyde dehydrogenase; nadp specific 8 glutamate semialdehyde dehydrogenase; nadp specific 8-glutamate semialdehyde dehydrogenase; 1 pyrroline 5 carboxylate dehydrogenase;

MeSH Related Number : 9054-82-4 (CRN);

Registry Number MeSH : EC 1.5.1.12; EC 1.2.1.88;

Wikipedia link : https://en.wikipedia.org/wiki/1-pyrroline-5-carboxylate dehydrogenase;

Is substance : O;

UNII : EC 1.2.1.88;

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An enzyme that catalyzes the oxidation of 1-pyrroline-5-carboxylate to L-GLUTAMATE in the presence of NAD. Defects in the enzyme are the cause of hyperprolinemia II.

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01/05/2025


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