Preferred Label : Shy-Drager syndrome;
MeSH definition : A progressive neurodegenerative condition of the central and autonomic nervous systems
characterized by atrophy of the preganglionic lateral horn neurons of the thoracic
spinal cord. This disease is generally considered a clinical variant of MULTIPLE SYSTEM
ATROPHY. Affected individuals present in the fifth or sixth decade with ORTHOSTASIS
and bladder dysfunction; and later develop FECAL INCONTINENCE; anhidrosis; ATAXIA;
IMPOTENCE; and alterations of tone suggestive of basal ganglia dysfunction. (From
Adams et al., Principles of Neurology, 6th ed, p536);
MeSH synonym : dysautonomic orthostatic hypotensions; dysautonomia orthostatic hypotension syndrome; progressive autonomic failures; dysautonomic orthostatic hypotension; failure, progressive autonomic; hypotension, dysautonomic orthostatic; idiopathic orthostatic hypotension, shy drager type; hypotensions, dysautonomic orthostatic; syndrome, shy-drager; syndrome, dysautonomia-orthostatic hypotension; syndrome, dysautonomia orthostatic hypotension; orthostatic hypotension, dysautonomic; orthostatic hypotensions, dysautonomic; dysautonomia-orthostatic hypotension syndrome; dysautonomia-orthostatic hypotension syndromes; hypotension syndrome, dysautonomia-orthostatic; hypotension syndromes, dysautonomia-orthostatic; syndromes, dysautonomia-orthostatic hypotension; autonomic failure, progressive; autonomic failures, progressive; failures, progressive autonomic; progressive autonomic failure; idiopathic orthostatic hypotension, shy-drager type; shy drager syndrome;
CISMeF synonym : Shy-Drager; Shy Drager; Shy-Drager's syndrome;
Wikipedia link : https://en.wikipedia.org/wiki/Shy-drager syndrome;
Origin ID : D012791;
UMLS CUI : C0037019;
Allowable qualifiers
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- Currated CISMeF NLP mapping
- DO Cross reference
- Manual NTBT mappings (CISMeF)
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- See also
- Semantic type(s)
- UMLS correspondences (same concept)
A progressive neurodegenerative condition of the central and autonomic nervous systems
characterized by atrophy of the preganglionic lateral horn neurons of the thoracic
spinal cord. This disease is generally considered a clinical variant of MULTIPLE SYSTEM
ATROPHY. Affected individuals present in the fifth or sixth decade with ORTHOSTASIS
and bladder dysfunction; and later develop FECAL INCONTINENCE; anhidrosis; ATAXIA;
IMPOTENCE; and alterations of tone suggestive of basal ganglia dysfunction. (From
Adams et al., Principles of Neurology, 6th ed, p536)
