" /> Hamman-Rich Syndrome - CISMeF





Preferred Label : Hamman-Rich Syndrome;

MeSH definition : Acute idiopathic interstitial pneumonitis characterized by diffuse PULMONARY ALVEOLI damage with uniform edematous connective tissue proliferation. It is often associated with extensive fibroblastic distortion of the lung parenchyma and leads to ADULT RESPIRATORY DISTRESS SYNDROME in later stages.;

MeSH synonym : Hamman Rich Syndrome; Acute Interstitial Pneumonia; Acute Interstitial Pneumonias; Interstitial Pneumonia, Acute; Pneumonia, Acute Interstitial; Acute Interstitial Pneumonitis; Acute Interstitial Pneumonitides; Interstitial Pneumonitis, Acute; Pneumonitis, Acute Interstitial; Hamman-Rich Disease; Hamman Rich Disease;

Wikipedia link : https://en.wikipedia.org/wiki/Acute interstitial pneumonitis;

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Acute idiopathic interstitial pneumonitis characterized by diffuse PULMONARY ALVEOLI damage with uniform edematous connective tissue proliferation. It is often associated with extensive fibroblastic distortion of the lung parenchyma and leads to ADULT RESPIRATORY DISTRESS SYNDROME in later stages.

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29/07/2025


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