Cholangitis, primary sclerosing

Preferred Label : Cholangitis, primary sclerosing;

Symbol : PSC;

CISMeF acronym : PSC;

Type : Phenotype or locus, molecular basis unknown;

Description : Primary sclerosing cholangitis (PSC) is a slowly progressive cholestatic liver disease characterized by fibroobliterative inflammation of the biliary tract, leading to cirrhosis and portal hypertension. It is a major indication for liver transplantation (Sheth et al., 2003). Approximately 75 to 80% of PSC cases are associated with inflammatory bowel disease (IBD; see 266600), and 2.5 to 7.5% of patients with IBD develop PSC (Lee and Kaplan, 1995).;

Prefixed ID : %613806;

Details

Origin ID

613806;

UMLS CUI

C0566602;

Automatic exact mappings (from CISMeF team)
- Pancreatic Stellate Cell [NCIt concept]
- cellulose sodium phosphate [SNOMED Notion]
Currated CISMeF NLP mapping
- Primary Sclerosing Cholangitis [NCIt concept]
- Primary sclerosing cholangitis [ICD-11 Subcategory]
- Primary sclerosing cholangitis [MeSH concept]
- Primary sclerosing cholangitis [ORDO Disease]
- Primary sclerosing cholangitis [MedDRA LLT]
- Primary sclerosing cholangitis (disorder) [Inactive SNOMED CT concept]
- Primary sclerosing cholangitis (disorder) [SNOMED CT concept]
- cholangitis, sclerosing [MeSH concept]
- primary sclerosing cholangitis [DO Concept]
- primary sclerosing cholangitis [Disease (Nov.)]
- primary sclerosing cholangitis [Radlex concept]
- primary sclerosing cholangitis [SNOMED Notion]
DO Cross reference
- primary sclerosing cholangitis [DO Concept]
False automatic mappings
- Posterior Subcapsular Cataract [NCIt concept]
ORDO concept(s)
- Primary sclerosing cholangitis [ORDO Disease]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
UMLS correspondences (same concept)
- Primary Sclerosing Cholangitis [NCIt concept]
- Primary sclerosing cholangitis [ORDO Disease]
- Primary sclerosing cholangitis [MeSH concept]
- Primary sclerosing cholangitis [MedDRA LLT]
- Primary sclerosing cholangitis (disorder) [SNOMED CT concept]
- primary sclerosing cholangitis [SNOMED Notion]
- primary sclerosing cholangitis [Radlex concept]
- primary sclerosing cholangitis [DO Concept]
Validated automatic mappings to NTBT
- cholangitis, sclerosing [MeSH Descriptor]
- sclerosing cholangitis [Disease (Nov.)]

Keyword's position in hierarchy(ies) :

You can consult :

recommendations
documents concerning education
documents for patients