Membranoproliferative glomerulonephritis, X-linked

Preferred Label : Membranoproliferative glomerulonephritis, X-linked;

Type : Other, mainly phenotypes with suspected mendelian basis;

Alternative titles and symbols : Mesangiocapillary glomerulonephritis, X-linked;

Description : Habib et al. (1973) recognized 2 morphologic classes for the glomerular changes seen in patients with mesangiocapillary (membranoproliferative) glomerulonephritis (MPGN). Type I is characterized by double contour appearance of the capillary walls due to mesangial cell interposition, with nonargyrophilic subendothelial deposits which are finely granular on electron microscopy. Type II is characterized by linear dense deposits within the basement membrane and only rare double contours. These 2 types appear to be distinct with no conversion of one type to another on serial biopsy. Strife et al. (1977) described a third variety in which there are not only subendothelial deposits but also numerous subepithelial and intramembranous deposits, associated with replication of the lamina densa and frequently disruption of the whole basement membrane.;

Inheritance : ? X-linked predisposition;

Prefixed ID : 305800;

Details

Origin ID

305800;

UMLS CUI

C1844501;

Currated CISMeF NLP mapping
- Glomerular disease with membranoproliferative glomerular changes [ICD-11 More detail]
- Glomerulonephritis membranoproliferative [MedDRA Preferred Term]
- Membranoproliferative Glomerulonephritis [NCIt concept]
- Membranoproliferative glomerulonephritis [HPO term]
- Membranoproliferative glomerulonephritis [MedDRA LLT]
- Mesangial proliferative glomerulonephritis [PASCAL descriptor]
- Mesangiocapillary glomerulonephritis (disorder) [SNOMED CT concept]
- glomerulonephritis, membranoproliferative [MeSH concept]
- glomerulonephritis, membranoproliferative [MeSH Descriptor]
- membranoproliferative glomerulonephritis, X-Linked [MeSH concept]
- membranoproliferative glomerulonephritis, X-Linked [MeSH Supplementary Concept]
- mesangiocapillary glomerulonephritis, nos [SNOMED Notion]
DO Cross reference
- membranoproliferative glomerulonephritis [DO Concept]
HPO term(s)
- Abnormality of metabolism/homeostasis [HPO term]
- Cardiac shunt [HPO term]
- Lipodystrophy [HPO term]
- Membranoproliferative glomerulonephritis [HPO term]
ORDO concept(s)
- Primary membranoproliferative glomerulonephritis [ORDO Disease]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
UMLS correspondences (same concept)
- membranoproliferative glomerulonephritis, X-Linked [MeSH Supplementary Concept]
- membranoproliferative glomerulonephritis, X-Linked [MeSH concept]

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