Alternative titles and symbols : Complex V, atp synthase, subunit atpase 6; ATP6;
Description : Complex V (ATP synthase) of the mitochondrion comprises 10-16 subunits encoded by
nuclear DNA and 2 subunits (ATPase 6 and ATPase 8) encoded by mtDNA. Subunit 6 of
mitochondrial ATP synthase (complex V) is encoded by nucleotides 8527-9207 of the
mitochondrial genome. For a discussion of genetic heterogeneity of mitochondrial complex
V (ATP synthase) deficiency, see 614053.;