ICD-11 code : 4A41.1;
Preferred Label : Polymyositis;
ICD-11 definition : Polymyositis is an inflammatory muscle disease of unknown aetiology occurring predominantly
in adults and characterised clinically by proximal muscle weakness (shoulders, arms,
thighs), often with associated myalgia. Involvement of pharyngeal and oesophageal
muscles may result in dysphagia and a risk of aspiration pneumonia. Myocarditis with
rhythm disturbances or cardiomyopathy is a rare but serious complication. Polymyositis
may be associated with other autoimmune diseases, malignancy or viral infection. Although
serum muscle enzyme concentrations and electromyography are usually abnormal, definitive
diagnosis requires demonstration of characteristic histological changes, including
muscle necrosis, muscle fibre regeneration and diffuse infiltration by CD8 T lymphocytes,
on muscle biopsy.;
ICD-11 synonym : PM - [polymyositis];
ICD-11 acronym : PM;
ICD-11 "other" category code : 4A41.1Y;
ICD-11 "unspecified" category code : 4A41.1Z;
Origin ID : 1157134196;
UMLS CUI : C0085655;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
False automatic mappings
ICD-10 Mapping
Semantic type(s)
UMLS correspondences (same concept)
Polymyositis is an inflammatory muscle disease of unknown aetiology occurring predominantly
in adults and characterised clinically by proximal muscle weakness (shoulders, arms,
thighs), often with associated myalgia. Involvement of pharyngeal and oesophageal
muscles may result in dysphagia and a risk of aspiration pneumonia. Myocarditis with
rhythm disturbances or cardiomyopathy is a rare but serious complication. Polymyositis
may be associated with other autoimmune diseases, malignancy or viral infection. Although
serum muscle enzyme concentrations and electromyography are usually abnormal, definitive
diagnosis requires demonstration of characteristic histological changes, including
muscle necrosis, muscle fibre regeneration and diffuse infiltration by CD8 T lymphocytes,
on muscle biopsy.