" /> Severe combined immunodeficiencies - CISMeF





ICD-11 code : 4A01.10;

Preferred Label : Severe combined immunodeficiencies;

ICD-11 definition : Severe combined immunodeficiency (SCID) comprises a group of rare monogenic primary immunodeficiency disorders characterized by a lack of functional peripheral T lymphocytes resulting in early-onset severe respiratory infections and failure to thrive.;

ICD-11 synonym : SCID - [Severe combined immunodeficiencies];

ICD-11 acronym : SCID;

ICD-11 inclusion : severe combined immunodeficiency disease;

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Severe combined immunodeficiency (SCID) comprises a group of rare monogenic primary immunodeficiency disorders characterized by a lack of functional peripheral T lymphocytes resulting in early-onset severe respiratory infections and failure to thrive.

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30/07/2025


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