ICD-11 definition : Ichthyosis vulgaris accounts for 95% of all cases of hereditary ichthyosis. It is
an autosomal dominant condition due to filaggrin gene mutations. At birth the skin
may appear normal but it gradually becomes dry, rough and scaly, with most signs and
symptoms appearing by the age of 5. Ichthyosis vulgaris can affect all parts of the
skin surface including the face and scalp though the limb flexures are usually spared.
Hyperlinearity of the palms is a characteristic feature. It is closely associated
with the development of atopic eczema.;
Ichthyosis vulgaris accounts for 95% of all cases of hereditary ichthyosis. It is
an autosomal dominant condition due to filaggrin gene mutations. At birth the skin
may appear normal but it gradually becomes dry, rough and scaly, with most signs and
symptoms appearing by the age of 5. Ichthyosis vulgaris can affect all parts of the
skin surface including the face and scalp though the limb flexures are usually spared.
Hyperlinearity of the palms is a characteristic feature. It is closely associated
with the development of atopic eczema.