ICD-11 definition : Biliary atresia is a rare disease characterised by an inflammatory biliary obstruction
of unknown origin that presents in the neonatal period. It is the most frequent surgical
cause of cholestatic jaundice in this age group. Untreated, this condition leads to
cirrhosis and death within the first years of life.;
ICD-11 synonym : Atresia of bile ducts; BA - [biliary atresia]; congenital bile duct atresia; impervious bile duct; bile duct atresia; congenital biliary atresia;
ICD-11 acronym : BA;
ICD-11 inclusion : cystic duct atresia; biliary duct atresia; bile ductal atresia; atresia of common duct;
Biliary atresia is a rare disease characterised by an inflammatory biliary obstruction
of unknown origin that presents in the neonatal period. It is the most frequent surgical
cause of cholestatic jaundice in this age group. Untreated, this condition leads to
cirrhosis and death within the first years of life.