ICD-11 code : 4A41.10;
Preferred Label : Juvenile polymyositis;
ICD-11 definition : Juvenile polymyositis is a rare childhood idiopathic inflammatory myopathy. It is
frequently misdiagnosed, as it lacks a unique clinical phenotype. Traditionally, it
presents with weakness of the proximal muscles that evolves over weeks to months.
The primary histologic features are fibre size variability, scattered necrotic and
regenerating fibres, and perivascular and endomysial cellular infiltrates.;
Origin ID : 633330307;
Currated CISMeF NLP mapping
- ICD-10 Mapping
Juvenile polymyositis is a rare childhood idiopathic inflammatory myopathy. It is
frequently misdiagnosed, as it lacks a unique clinical phenotype. Traditionally, it
presents with weakness of the proximal muscles that evolves over weeks to months.
The primary histologic features are fibre size variability, scattered necrotic and
regenerating fibres, and perivascular and endomysial cellular infiltrates.
