ICD-11 code : 4A41.10;
Preferred Label : Juvenile polymyositis;
ICD-11 definition : Juvenile polymyositis is a rare childhood idiopathic inflammatory myopathy. It is
frequently misdiagnosed, as it lacks a unique clinical phenotype. Traditionally, it
presents with weakness of the proximal muscles that evolves over weeks to months.
The primary histologic features in are fiber size variability, scattered necrotic
and regenerating fibers, and perivascular and endomysial cellular infiltrates.;
Origin ID : 633330307;
Currated CISMeF NLP mapping
- ICD-10 Mapping
Juvenile polymyositis is a rare childhood idiopathic inflammatory myopathy. It is
frequently misdiagnosed, as it lacks a unique clinical phenotype. Traditionally, it
presents with weakness of the proximal muscles that evolves over weeks to months.
The primary histologic features in are fiber size variability, scattered necrotic
and regenerating fibers, and perivascular and endomysial cellular infiltrates.
