ICD-11 code : EB90.42;
Preferred Label : Calcific arteriolopathy;
ICD-11 definition : Calcific arteriolopathy (calciphylaxis) is a life-threatening vasculopathic disorder
characterized by painful cutaneous ischaemia and infarction due to calcification,
intimal fibroplasia, and thrombosis of subcutaneous arterioles. It is most commonly
associated with end-stage kidney disease or renal transplantation, particularly in
the context of longstanding diabetes mellitus. Affected skin, commonly on the hips
and thighs, appears mottled, grey and devitalized before progressing to full thickness
infarction and deep ulceration. These changes may be accompanied by indurated subcutaneous
plaques indicating an underlying calcifying panniculitis. The condition may be but
is not always associated with hyperparathyroidism or an elevated calcium-phosphate
product.;
ICD-11 synonym : Calciphylaxis; calcific arteriopathy;
ICD-11 inclusion : Calciphylaxis;
Origin ID : 574291789;
Automatic exact mappings (from CISMeF team)
- ICD-10 Mapping
- Validated automatic mappings to BTNT
Calcific arteriolopathy (calciphylaxis) is a life-threatening vasculopathic disorder
characterized by painful cutaneous ischaemia and infarction due to calcification,
intimal fibroplasia, and thrombosis of subcutaneous arterioles. It is most commonly
associated with end-stage kidney disease or renal transplantation, particularly in
the context of longstanding diabetes mellitus. Affected skin, commonly on the hips
and thighs, appears mottled, grey and devitalized before progressing to full thickness
infarction and deep ulceration. These changes may be accompanied by indurated subcutaneous
plaques indicating an underlying calcifying panniculitis. The condition may be but
is not always associated with hyperparathyroidism or an elevated calcium-phosphate
product.
