ICD-11 code : 3A10.00;
Preferred Label : Haemolytic anaemia due to glucose-6-phosphate dehydrogenase deficiency;
ICD-11 definition : Glucose-6-phosphate dehydrogenase (G6PD) deficiency is the most common hereditary
erythrocyte enzyme deficiency that can manifest with severe neonatal jaundice which
can lead to serious neurological consequences, or, most often, with acute hemolytic
anemia following ingestion of certain foods (fava beans), common drugs (some antimalaria
drugs, sulphamides, analgesics), or in the course of an infection, in otherwise asymptomatic
individuals.;
ICD-11 synonym : G6PD anaemia; anaemia due to glucose-6-phosphate dehydrogenase deficiency; glucose-6-phosphate dehydrogenase deficiency with anaemia; Favism; Chronic non spherocytic anaemia; G6PD - [glucose-6-phosphate dehydrogenase deficiency] anaemia; glucose-6-phosphate dehydrogenase deficiency anaemia; favism anaemia; Haemolytic anaemia due toG6PD deficiency;
Origin ID : 506935822;
Currated CISMeF NLP mapping
ICD-10 Mapping
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Validated automatic mappings to BTNT
Validated automatic mappings to NTBT
Glucose-6-phosphate dehydrogenase (G6PD) deficiency is the most common hereditary
erythrocyte enzyme deficiency that can manifest with severe neonatal jaundice which
can lead to serious neurological consequences, or, most often, with acute hemolytic
anemia following ingestion of certain foods (fava beans), common drugs (some antimalaria
drugs, sulphamides, analgesics), or in the course of an infection, in otherwise asymptomatic
individuals.