Ebstein malformation of tricuspid valve

ICD-11 code : LA87.03;

Preferred Label : Ebstein malformation of tricuspid valve;

ICD-11 definition : A congenital cardiovascular malformation of the tricuspid valve and right ventricle that is characterised by incomplete delamination of the septal and inferior (posterior) tricuspid valvar leaflets from the myocardium of the right ventricle, and varying degrees of downward (apical) rotational displacement of the functional annulus. Additional information: associated cardiac anomalies include an interatrial communication, the presence of accessory conduction pathways and varying degrees of right ventricular outflow tract obstruction, including pulmonary atresia. In the setting of discordant atrioventricular and ventriculo-arterial connections ['Congenitally corrected transposition of great arteries'], 'Ebstein malformation of tricuspid valve' may be present.;

ICD-11 synonym : congenital Ebstein deformity of tricuspid valve; Ebstein cardiopathy; Ebstein syndrome; Ebstein anomaly; Ebstein disease; Accessory tricuspid valve tissue; ebstein anomaly of tricuspid valve;

Details

Origin ID

307157712;

UMLS CUI

C0013481;

Automatic exact mappings (from CISMeF team)
- Accessory tricuspid valve tissue [ORDO Disease]
- Ebstein's anomaly of common atrioventricular valve (disorder) [SNOMED CT concept]
Currated CISMeF NLP mapping
- Ebstein Anomaly [NCIt concept]
- Ebstein anomaly [DO Concept]
- Ebstein anomaly [Radlex concept]
- Ebstein anomaly [OMIM Phenotype]
- Ebstein anomaly of the tricuspid valve [HPO term]
- Ebstein anomaly of the tricuspid valve [PASCAL descriptor]
- Ebstein malformation of the tricuspid valve [ORDO Disease]
- Ebstein's anomaly [MedDRA Preferred Term]
- Ebstein's anomaly [ICD-10 Sub-category]
- Ebstein's anomaly [ICD-9 code]
- Ebstein's anomaly of tricuspid valve (disorder) [SNOMED CT concept]
- Ebsteins anomaly [ICD-10 Sub-category (who)]
- ebstein anomaly [MeSH concept]
- ebstein anomaly [MeSH Descriptor]
- ebstein's anomaly [SNOMED Notion]
ICD-10 Mapping
- Ebstein's anomaly [ICD-10 Sub-category]
See also inter- (CISMeF)
- Congenital accessory tissue of tricuspid valve (disorder) [SNOMED CT concept]
Semantic type(s)
- Congenital Abnormality [UMLS semantic type]
UMLS correspondences (same concept)
- Ebstein Anomaly [NCIt concept]
- Ebstein anomaly [DO Concept]
- Ebstein anomaly [OMIM Phenotype]
- Ebstein anomaly [Disease (Nov.)]
- Ebstein anomaly [Radlex concept]
- Ebstein anomaly of the tricuspid valve [HPO term]
- Ebstein malformation of the tricuspid valve [ORDO Disease]
- Ebstein's anomaly [ICD-9 code]
- Ebstein's anomaly [ICD-10 Sub-category]
- Ebstein's anomaly [MedDRA Preferred Term]
- Ebstein's anomaly of tricuspid valve (disorder) [SNOMED CT concept]
- ebstein anomaly [MeSH Descriptor]
- ebstein anomaly [MeSH concept]
- ebstein's anomaly [SNOMED Notion]

Keyword's position in hierarchy(ies) :

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