ICD-11 code : FB86.10;
Preferred Label : Hypertrophic osteoarthropathy;
ICD-11 definition : Hypertrophic osteoarthropathy (HOA) is a syndrome of clubbing of the digits, subperiosteal
new bone formation (periostitis) affecting the long bones, and arthritis. The primary
hereditary form is associated with mutations in the HPGD gene. The secondary form
may be secondary to a number of systemic disorders, most commonly as a paraneoplastic
phenomenon related to bronchial carcinoma.;
ICD-11 synonym : Marie-Bamberger disease; Bamberger-Marie syndrome;
Origin ID : 218751696;
Automatic exact mappings (from CISMeF team)
- ICD-10 Mapping
Hypertrophic osteoarthropathy (HOA) is a syndrome of clubbing of the digits, subperiosteal
new bone formation (periostitis) affecting the long bones, and arthritis. The primary
hereditary form is associated with mutations in the HPGD gene. The secondary form
may be secondary to a number of systemic disorders, most commonly as a paraneoplastic
phenomenon related to bronchial carcinoma.
