" /> Double outlet right ventricle with subpulmonary ventricular septal defect, transposition type - CISMeF





ICD-11 code : LA85.20;

Preferred Label : Double outlet right ventricle with subpulmonary ventricular septal defect, transposition type;

ICD-11 definition : A congenital cardiovascular malformation that is a variant of double outlet right ventricle with concordant atrioventricular connections that is associated with a subpulmonary ventricular septal defect (includes Taussig-Bing heart).;

ICD-11 synonym : double outlet right ventricle with subpulmonary interventricular communication, transposition type; Taussig-Bing syndrome; Taussig-Bing heart; Taussig-Bing malformation;

ICD-11 inclusion : Taussig-Bing; Taussig-Bing defect; Taussig-Bing complex;

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A congenital cardiovascular malformation that is a variant of double outlet right ventricle with concordant atrioventricular connections that is associated with a subpulmonary ventricular septal defect (includes Taussig-Bing heart).

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03/02/2026


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