ICD-11 code : LD26.41;
Preferred Label : Arthrogryposis multiplex congenita;
ICD-11 definition : Arthrogryposis multiplex congenita, comprises nonprogressive congenital conditions
characterized by multiple joint contractures. The term is currently used in connection
with a very heterogeneous group of disorders that all include multiple congenital
joint contractures. The major cause of arthrogryposis is fetal akinesia due to fetal
abnormalities (e.g. neurogenic, muscle, or connective tissue abnormalities; mechanical
limitations to movement) or maternal disorders (e.g. infection, drugs, trauma, other
maternal illnesses). Generalized fetal akinesia can also lead to polyhydramnios, pulmonary
hypoplasia, micrognathia, ocular hypertelorism, and short umbilical cord. Lack of
fetal movement causes extra connective tissue to develop around the joint, limiting
movement and further aggravating the joint contracture.;
ICD-11 synonym : AMC - [arthrogryposis multiplex congenita]; congenital multiple arthrogryposis; congenital multiplex arthrogryposis; congenital amyoplasia; amyoplasia congenita;
ICD-11 acronym : AMC;
Origin ID : 1930990330;
Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
- False automatic mappings
- ICD-10 Mapping
Arthrogryposis multiplex congenita, comprises nonprogressive congenital conditions
characterized by multiple joint contractures. The term is currently used in connection
with a very heterogeneous group of disorders that all include multiple congenital
joint contractures. The major cause of arthrogryposis is fetal akinesia due to fetal
abnormalities (e.g. neurogenic, muscle, or connective tissue abnormalities; mechanical
limitations to movement) or maternal disorders (e.g. infection, drugs, trauma, other
maternal illnesses). Generalized fetal akinesia can also lead to polyhydramnios, pulmonary
hypoplasia, micrognathia, ocular hypertelorism, and short umbilical cord. Lack of
fetal movement causes extra connective tissue to develop around the joint, limiting
movement and further aggravating the joint contracture.
