ICD-11 code : 4A01.01;
Preferred Label : Immunodeficiencies with severe reduction in at least two serum immunoglobulin isotypes
with normal or low numbers of B cells;
ICD-11 definition : This refers to a nonfamilial type of primary immune deficiency disease characterized
by a reduction in at least two serum immunoglobulin isotypes. Circulating B cells
may be normal or low.;
ICD-11 synonym : common variable immune deficiency; nonfamilial hypogammaglobulinaemia;
ICD-11 inclusion : hypogammaglobulinaemia antibody deficiency syndrome; Agammaglobulinaemia with immunoglobulin-bearing B-lymphocytes; acquired agammaglobulinaemia; Hypogammaglobulinaemia NOS; agammaglobulinaemia; hypogammaglobulinaemia; common variable agammaglobulinaemia; immunoglobulin-bearing b-lymphocytes agammaglobulinaemia; agammaglobulinaemia NOS; nonfamilial agammaglobulinaemia; agammaglobulinaemia antibody deficiency syndrome;
Origin ID : 1915135976;
Automatic exact mappings (from CISMeF team)
ICD-10 Mapping
This refers to a nonfamilial type of primary immune deficiency disease characterized
by a reduction in at least two serum immunoglobulin isotypes. Circulating B cells
may be normal or low.