ICD-11 code : 5C50.E0;
Preferred Label : Classical organic aciduria;
ICD-11 definition : This a term used to classify a group of metabolic disorders which disrupt normal amino
acid metabolism, particularly branched-chain amino acids, causing a buildup of acids
which are usually not present.;
Origin ID : 1879509617;
Currated CISMeF NLP mapping
ICD-10 Mapping
Validated automatic mappings to NTBT
This a term used to classify a group of metabolic disorders which disrupt normal amino
acid metabolism, particularly branched-chain amino acids, causing a buildup of acids
which are usually not present.