ICD-11 code : 5C64.20;
Preferred Label : Acrodermatitis enteropathica;
ICD-11 definition : Acrodermatitis enteropathica is an uncommon autosomal recessive disorder of intestinal
zinc absorption. Signs usually appear within the first months of life with an exudative
and crusted erythema located predominantly around body orifices (mouth, anogenital)
and on the scalp and distal extremities. The signs are often misdiagnosed as being
due to infection. The condition responds rapidly to zinc supplementation which must
be continued throughout life.;
ICD-11 synonym : Danbolt-Closs syndrome; Brandt syndrome; primary zinc malabsorption syndrome;
Origin ID : 1813939482;
Currated CISMeF NLP mapping
ICD-10 Mapping
Validated automatic mappings to NTBT
Acrodermatitis enteropathica is an uncommon autosomal recessive disorder of intestinal
zinc absorption. Signs usually appear within the first months of life with an exudative
and crusted erythema located predominantly around body orifices (mouth, anogenital)
and on the scalp and distal extremities. The signs are often misdiagnosed as being
due to infection. The condition responds rapidly to zinc supplementation which must
be continued throughout life.