ICD-11 code : LD27.03;
Preferred Label : Hidrotic ectodermal dysplasia, Clouston type;
ICD-11 definition : Clouston syndrome (or hidrotic ectodermal dysplasia) is an inherited disorder characterised
by the clinical triad of nail dystrophy, alopecia, and palmoplantar hyperkeratosis.;
ICD-11 synonym : Clouston syndrome (MIM 129500); Clouston syndrome;
Origin ID : 1811429982;
Automatic exact mappings (from CISMeF team)
ICD-10 Mapping
Clouston syndrome (or hidrotic ectodermal dysplasia) is an inherited disorder characterised
by the clinical triad of nail dystrophy, alopecia, and palmoplantar hyperkeratosis.