ICD-11 code : LA8B.22;
Preferred Label : Interrupted aortic arch;
ICD-11 definition : A congenital cardiovascular malformation in which there is an absence of luminal continuity
between the ascending and descending aorta. Additional information: this includes
luminal atresia with discontinuity between the aortic segments and also luminal atresia
with fibrous continuity between the aortic segments. Interrupted aortic arch is defined
as the loss of luminal continuity between the ascending and descending aorta. In most
cases, blood flow to the descending thoracic aorta is through a patent arterial duct,
and there is a large ventricular septal defect. Arch interruption is further defined
by site of interruption. In type A, interruption is distal to the left subclavian
artery; in type B, interruption is between the left carotid and left subclavian arteries;
and in type C, interruption occurs between the innominate and left carotid arteries.;
ICD-11 synonym : aortic arch interruption; IAA - [interrupted aortic arch]; aorta atresia;
ICD-11 acronym : IAA;
ICD-11 inclusion : aorta arch atresia; aortic arch atresia; aorta ring atresia; aortic ring atresia;
Origin ID : 1769930414;
Automatic exact mappings (from CISMeF team)
- ICD-10 Mapping
A congenital cardiovascular malformation in which there is an absence of luminal continuity
between the ascending and descending aorta. Additional information: this includes
luminal atresia with discontinuity between the aortic segments and also luminal atresia
with fibrous continuity between the aortic segments. Interrupted aortic arch is defined
as the loss of luminal continuity between the ascending and descending aorta. In most
cases, blood flow to the descending thoracic aorta is through a patent arterial duct,
and there is a large ventricular septal defect. Arch interruption is further defined
by site of interruption. In type A, interruption is distal to the left subclavian
artery; in type B, interruption is between the left carotid and left subclavian arteries;
and in type C, interruption occurs between the innominate and left carotid arteries.
