ICD-11 code : LA8B.22;
Preferred Label : Interrupted aortic arch;
ICD-11 definition : A congenital cardiovascular malformation in which there is an absence of luminal continuity
between the ascending and descending aorta. This includes luminal atresia with discontinuity
between the aortic segments and also luminal atresia with fibrous continuity between
the aortic segments. Interrupted aortic arch is defined as the loss of luminal continuity
between the ascending and descending aorta. In most cases, blood flow to the descending
thoracic aorta is through a patent arterial duct, and there is a large ventricular
septal defect. Arch interruption is further defined by site of interruption. In type
A, interruption is distal to the left subclavian artery; in type B, interruption is
between the left carotid and left subclavian arteries; and in type C, interruption
occurs between the innominate and left carotid arteries.;
ICD-11 synonym : aortic arch interruption; IAA - [interrupted aortic arch]; aorta atresia;
ICD-11 acronym : IAA;
ICD-11 inclusion : aorta arch atresia; aortic arch atresia; aorta ring atresia; aortic ring atresia;
Origin ID : 1769930414;
Automatic exact mappings (from CISMeF team)
- ICD-10 Mapping
A congenital cardiovascular malformation in which there is an absence of luminal continuity
between the ascending and descending aorta. This includes luminal atresia with discontinuity
between the aortic segments and also luminal atresia with fibrous continuity between
the aortic segments. Interrupted aortic arch is defined as the loss of luminal continuity
between the ascending and descending aorta. In most cases, blood flow to the descending
thoracic aorta is through a patent arterial duct, and there is a large ventricular
septal defect. Arch interruption is further defined by site of interruption. In type
A, interruption is distal to the left subclavian artery; in type B, interruption is
between the left carotid and left subclavian arteries; and in type C, interruption
occurs between the innominate and left carotid arteries.
