ICD-11 code : LA8A.23;
Preferred Label : Aortic valvar atresia;
ICD-11 definition : A congenital cardiovascular malformation in which there is no orifice of the aortic
valve. Additional information: aortic valvar atresia will most often not be coded
independently, as it is frequently included within the 'Hypoplastic left heart syndrome'
code as part of this spectrum of cardiovascular malformations. However, there is a
small subset of patients with aortic valve atresia who have a well developed left
ventricle and mitral valve and a large ventricular septal defect (nonrestrictive or
restrictive).;
ICD-11 synonym : aortic valve atresia; congenital atresia of aortic valve; aortic valvular atresia; imperforate aortic valve;
Origin ID : 1700740306;
Automatic exact mappings (from CISMeF team)
ICD-10 Mapping
A congenital cardiovascular malformation in which there is no orifice of the aortic
valve. Additional information: aortic valvar atresia will most often not be coded
independently, as it is frequently included within the 'Hypoplastic left heart syndrome'
code as part of this spectrum of cardiovascular malformations. However, there is a
small subset of patients with aortic valve atresia who have a well developed left
ventricle and mitral valve and a large ventricular septal defect (nonrestrictive or
restrictive).