ICD-11 code : LA8A.23;
Preferred Label : Aortic valvar atresia;
ICD-11 definition : A congenital cardiovascular malformation in which there is no orifice of aortic valve
Aortic valve atresia will most often be coded under the hypoplastic left heart syndrome/complex
diagnostic codes since it most often occurs as part of a spectrum of cardiovascular
malformations. However, there is a small subset of patients with aortic valve atresia
who have a well developed left ventricle and mitral valve and a large ventricular
septal defect (nonrestrictive or restrictive);
ICD-11 synonym : aortic valve atresia; congenital atresia of aortic valve; aortic valvular atresia; imperforate aortic valve;
Origin ID : 1700740306;
Automatic exact mappings (from CISMeF team)
ICD-10 Mapping
A congenital cardiovascular malformation in which there is no orifice of aortic valve
Aortic valve atresia will most often be coded under the hypoplastic left heart syndrome/complex
diagnostic codes since it most often occurs as part of a spectrum of cardiovascular
malformations. However, there is a small subset of patients with aortic valve atresia
who have a well developed left ventricle and mitral valve and a large ventricular
septal defect (nonrestrictive or restrictive)