Dubin-Johnson syndrome

ICD-11 code : 5C58.02;

Preferred Label : Dubin-Johnson syndrome;

ICD-11 definition : Dubin-Johnson syndrome (DJS) is a benign, inherited liver disorder characterized clinically by chronic, predominantly conjugated, hyperbilirubinemia and histopathologically by black-brown pigment deposition in parenchymal liver cells.;

ICD-11 synonym : DJS - [Dubin-Johnson syndrome]; Dubin-Sprinz disease; Hyperbilirubinaemia type 2; Sprinz-Nelson syndrome;

ICD-11 acronym : DJS;

Details

Origin ID

1691610999;

Automatic exact mappings (from CISMeF team)
- ABCC2 wt Allele [NCIt concept]
- ATP binding cassette subfamily C member 2 [ORDO Gene]
- Dubin-Johnson syndrome [DO Concept]
- Other disorders of bilirubin metabolism [ICD-10 Sub-category]
Currated CISMeF NLP mapping
- Dubin-Johnson Syndrome [NCIt concept]
- Dubin-Johnson disease [PASCAL descriptor]
- Dubin-Johnson syndrome [MedDRA Preferred Term]
- Dubin-Johnson syndrome [ORDO Disease]
- Dubin-Johnson syndrome (disorder) [SNOMED CT concept]
- Dubin-johnson syndrome [OMIM Phenotype]
- dubin-johnson syndrome [SNOMED Notion]
- jaundice, chronic idiopathic [MeSH Descriptor]
- jaundice, chronic idiopathic [MeSH concept]
ICD-10 Mapping
- Other disorders of bilirubin metabolism [ICD-10 Sub-category]

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