ICD-11 code : 4A44.92;
Preferred Label : IgA vasculitis;
ICD-11 definition : Vasculitis, with IgA1-dominant immune deposits, affecting small vessels (predominantly
capillaries, venules, or arterioles). Often involves skin and gut, and frequently
causes arthritis. Glomerulonephritis indistinguishable from IgA nephropathy may occur.;
ICD-11 synonym : Allergic purpura; Schönlein–Henoch purpura; HSP - (Henoch-Schönlein purpura); Henoch-Schönlein purpura; Anaphylactoid purpura; HSP -;
ICD-11 inclusion : Henoch-Schönlein purpura;
Origin ID : 1629105375;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
ICD-10 Mapping
Vasculitis, with IgA1-dominant immune deposits, affecting small vessels (predominantly
capillaries, venules, or arterioles). Often involves skin and gut, and frequently
causes arthritis. Glomerulonephritis indistinguishable from IgA nephropathy may occur.