ICD-11 code : LD2F.14;
Preferred Label : MURCS association;
ICD-11 definition : MURCS association, which stands for Müllerian duct aplasia (MU), congenital renal
dysplasia (R), cervical somite anomalies (CS), is the atypical (or type II) form of
Mayer-Rokitansky-Küster-Hauser syndrome, characterized by utero-vaginal atresia in
otherwise normal females as well associated kidney and skeletal abnormalities and
hearing problems.;
ICD-11 synonym : Mayer-Rokitansky-Küster-Hauser syndrome type 2; Müllerian aplasia - renal aplasia - cervicothoracic somite dysplasia; MRKH syndrome type 2; Klippel-Feil deformity - conductive deafness - absent vagina;
Origin ID : 1521808255;
Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
- ICD-10 Mapping
MURCS association, which stands for Müllerian duct aplasia (MU), congenital renal
dysplasia (R), cervical somite anomalies (CS), is the atypical (or type II) form of
Mayer-Rokitansky-Küster-Hauser syndrome, characterized by utero-vaginal atresia in
otherwise normal females as well associated kidney and skeletal abnormalities and
hearing problems.
