ICD-11 code : 8A00.10;
Preferred Label : Progressive supranuclear palsy;
ICD-11 definition : Progressive supranuclear palsy (PSP) is a rare late-onset neurodegenerative disease
characterized by supranuclear gaze palsy, postural instability, progressive rigidity,
and mild dementia. Five clinical variants have been described with clinicopathological
correlations: Classical PSP (Richardson's syndrome), and four atypical variants of
PSP including PSP-Parkinsonism (PSP-P), PSP-Pure akinesia with gait freezing (PSP-PAGF),
PSP-corticobasal syndrome (PSP-CBS), and PSP-progressive non fluent aphasia (PSP-PNFA).;
ICD-11 synonym : Steele-Richardson-Olszewksi syndrome;
Origin ID : 1493396558;
Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
- ICD-10 Mapping
Progressive supranuclear palsy (PSP) is a rare late-onset neurodegenerative disease
characterized by supranuclear gaze palsy, postural instability, progressive rigidity,
and mild dementia. Five clinical variants have been described with clinicopathological
correlations: Classical PSP (Richardson's syndrome), and four atypical variants of
PSP including PSP-Parkinsonism (PSP-P), PSP-Pure akinesia with gait freezing (PSP-PAGF),
PSP-corticobasal syndrome (PSP-CBS), and PSP-progressive non fluent aphasia (PSP-PNFA).
