ICD-11 definition : Neurofibromatosis type 2 (NF2) is a tumor-prone disorder characterized by the development
of multiple schwannomas and meningiomas.;
ICD-11 synonym : Bilateral acoustic neurofibromatosis; NF2 - [Neurofibromatosis type 2] (MIM 101000); Familial acoustic neuroma; Familial vestibular schwannoma; Neurofibromatosis, central type; NF2 - [Neurofibromatosis type 2];