ICD-11 definition : Juvenile dermatomyositis is the early-onset form of dermatomyositis, a systemic autoimmune
inflammatory muscle disorder, characterized by proximal muscle weakness, evocative
skin lesion, and systemic manifestations.;
ICD-11 inclusion : juvenile myositis; childhood type dermatomyositis;
Juvenile dermatomyositis is the early-onset form of dermatomyositis, a systemic autoimmune
inflammatory muscle disorder, characterized by proximal muscle weakness, evocative
skin lesion, and systemic manifestations.