ICD-11 code : 1F2E.1;
Preferred Label : Disseminated paracoccidioidomycosis;
ICD-11 definition : Disseminated paracoccidioidomycosis results from haematogenous and lymphatic dissemination
of yeasts from the lungs and aerodigestive tract. Cutaneous involvement, seen in 25%
of cases, presents as crusted papules, ulcers, nodules, and verrucous plaques. Lymphadenopathy
occurs commonly in the cervical region, but all lymph node chains can be involved.
Adrenal glands are commonly affected with a significant risk of adrenal insufficiency
and Addisonian crisis. Long bones such as ribs, humeri, and clavicles can be involved.
Mesenteric lymph node involvement can lead to bowel obstruction. Meningoencephalitis
occurs in up to one quarter of cases.;
ICD-11 synonym : generalised paracoccidioidomycosis; Disseminated chronic paracoccidioidomycosis; South American disseminated blastomycosis;
Origin ID : 992933048;
UMLS CUI : C0276666;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
ICD-10 Mapping
Semantic type(s)
UMLS correspondences (same concept)
Disseminated paracoccidioidomycosis results from haematogenous and lymphatic dissemination
of yeasts from the lungs and aerodigestive tract. Cutaneous involvement, seen in 25%
of cases, presents as crusted papules, ulcers, nodules, and verrucous plaques. Lymphadenopathy
occurs commonly in the cervical region, but all lymph node chains can be involved.
Adrenal glands are commonly affected with a significant risk of adrenal insufficiency
and Addisonian crisis. Long bones such as ribs, humeri, and clavicles can be involved.
Mesenteric lymph node involvement can lead to bowel obstruction. Meningoencephalitis
occurs in up to one quarter of cases.