ICD-11 code : BC65.5;
Preferred Label : Catecholaminergic polymorphic ventricular tachycardia;
ICD-11 definition : Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a severe genetic arrhythmogenic
disorder of childhood characterized by adrenergically-induced ventricular tachycardia
(bidirectional ventricular tachycardia and, less frequently, supraventricular tachycardia
and atrial fibrillation) manifesting as syncope and sudden death.;
Origin ID : 976309888;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
ICD-10 Mapping
Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a severe genetic arrhythmogenic
disorder of childhood characterized by adrenergically-induced ventricular tachycardia
(bidirectional ventricular tachycardia and, less frequently, supraventricular tachycardia
and atrial fibrillation) manifesting as syncope and sudden death.