" /> Congenital anomaly of pulmonary arterial tree - CISMeF





ICD-11 code : LA8B.1;

Preferred Label : Congenital anomaly of pulmonary arterial tree;

ICD-11 definition : A congenital cardiovascular malformation of the pulmonary trunk (main pulmonary artery) and/or branch pulmonary arteries (right, left, and ramifications).;

ICD-11 synonym : Anomaly of pulmonary artery; Aberrant pulmonary artery;

ICD-11 inclusion : pulmonary arterial agenesis; pulmonary artery agenesis; pulmonary arterial origin anomaly; agenesis of pulmonary artery; pulmonary artery origin anomaly; pulmonary artery abnormality; Aberrant pulmonary artery; abnormal origin of pulmonary artery; Anomaly of pulmonary artery; pulmonary artery absent; congenital malposition of pulmonary artery;

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A congenital cardiovascular malformation of the pulmonary trunk (main pulmonary artery) and/or branch pulmonary arteries (right, left, and ramifications).

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02/01/2026


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