ICD-11 code : 9B71.3;
Preferred Label : Retinopathy of prematurity;
ICD-11 definition : Retinopathy of prematurity is a vasoproliferative disorder that affects extremely
premature infants potentially leading to severe visual impairment or blindness. Exposure
of newborn premature infants to hyperoxia down regulates retinal vascular endothelial
growth factor, Blood vessels constrict and can become obliterated, resulting in delays
of normal retinal vascular development. Low birth weight, young gestational age, and
severity of illness (e.g. respiratory distress syndrome, bronchopulmonary dysplasia,
sepsis) are associated factors. It primarily occurs in extremely low birth weight
infants because of the cessation of normal retinal vascular maturation.;
ICD-11 synonym : RLF- [retrolental fibroplasia]; retinopathy of prematurity NOS; ROP - [retinopathy of prematurity]; retrolental fibroplasia; Terry syndrome;
ICD-11 acronym : ROP; RLF;
ICD-11 inclusion : Retrolental fibroplasia;
Origin ID : 947283385;
UMLS CUI : C0035344;
Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
- ICD-10 Mapping
- See also inter- (CISMeF)
- Semantic type(s)
- UMLS correspondences (same concept)
Retinopathy of prematurity is a vasoproliferative disorder that affects extremely
premature infants potentially leading to severe visual impairment or blindness. Exposure
of newborn premature infants to hyperoxia down regulates retinal vascular endothelial
growth factor, Blood vessels constrict and can become obliterated, resulting in delays
of normal retinal vascular development. Low birth weight, young gestational age, and
severity of illness (e.g. respiratory distress syndrome, bronchopulmonary dysplasia,
sepsis) are associated factors. It primarily occurs in extremely low birth weight
infants because of the cessation of normal retinal vascular maturation.
