ICD-11 definition : Poikiloderma vasculare atrophicans is a cutaneous reaction pattern characterized by
mottled hyper- and hypomelanosis, telangiectasia and progressive dermal and epidermal
atrophy. It may manifest as a component of established mycosis fungoides but may precede
the development of the latter by many years and, in some cases, may persist indefinitely
without progression to frank lymphoma. It should be distinguished from other causes
of poikiloderma such as may be seen with dermatomyositis.;
Poikiloderma vasculare atrophicans is a cutaneous reaction pattern characterized by
mottled hyper- and hypomelanosis, telangiectasia and progressive dermal and epidermal
atrophy. It may manifest as a component of established mycosis fungoides but may precede
the development of the latter by many years and, in some cases, may persist indefinitely
without progression to frank lymphoma. It should be distinguished from other causes
of poikiloderma such as may be seen with dermatomyositis.