ICD-11 code : LA88.2;
Preferred Label : Tetralogy of Fallot;
ICD-11 definition : A group of congenital cardiovascular malformations with biventricular atrioventricular
alignments or connections characterised by anterosuperior deviation of the conal or
outlet septum or its fibrous remnant, narrowing or atresia of the pulmonary outflow,
a ventricular septal defect of the malalignment type, and biventricular origin of
the aorta. Additional information: tetralogy of Fallot will always have a ventricular
septal defect, narrowing or atresia of the pulmonary outflow, aortic override, and
most often right ventricular hypertrophy.;
ICD-11 synonym : Fallot tetralogy; tetrad of Fallot; subpulmonic stenosis, ventricular septal defect, overriding aorta, and right ventricular
hypertrophy; TOF - [tetralogy of fallot]; Fallot disease; Fallot tetrad; ventricular septal defect with pulmonary stenosis or atresia, dextraposition of aorta,
and hypertrophy of right ventricle; ventricular septal defect with obstructed right ventricular outflow.; Fallot complex;
ICD-11 acronym : TOF;
ICD-11 inclusion : ventricular hypertrophy in tetralogy of Fallot; ventricular septal defect in tetralogy of Fallot; dextraposition of aorta in Fallot tetralogy; ventricular septal defect in Fallot tetralogy; pulmonary stenosis in tetralogy of Fallot; tetralogy of Fallot with pulmonary stenosis; interventricular septal defect with dextroposition of aorta, pulmonary stenosis and
hypertrophy of right ventricle; interventricular septal defect, in tetralogy of Fallot;
ICD-11 "other" category code : LA88.2Y;
ICD-11 "unspecified" category code : LA88.2Z;
Origin ID : 90973426;
UMLS CUI : C0039685;
Currated CISMeF NLP mapping
- ICD-10 Mapping
- Semantic type(s)
- UMLS correspondences (same concept)
A group of congenital cardiovascular malformations with biventricular atrioventricular
alignments or connections characterised by anterosuperior deviation of the conal or
outlet septum or its fibrous remnant, narrowing or atresia of the pulmonary outflow,
a ventricular septal defect of the malalignment type, and biventricular origin of
the aorta. Additional information: tetralogy of Fallot will always have a ventricular
septal defect, narrowing or atresia of the pulmonary outflow, aortic override, and
most often right ventricular hypertrophy.
