ICD-11 code : LA88.2;
Preferred Label : Tetralogy of Fallot;
ICD-11 definition : A group of malformations with biventricular atrioventricular alignments or connections
characterized by anterosuperior deviation of the conal or outlet septum or its fibrous
remnant, narrowing or atresia of the pulmonary outflow, a ventricular septal defect
of the malalignment type, and biventricular origin of the aorta. Tetralogy of Fallot
will always have a ventricular septal defect, narrowing or atresia of the pulmonary
outflow, aortic override, and most often right ventricular hypertrophy.;
ICD-11 synonym : Fallot tetralogy; tetrad of Fallot; subpulmonic stenosis, ventricular septal defect, overriding aorta, and right ventricular
hypertrophy; TOF - [tetralogy of fallot]; Fallot disease; Fallot tetrad; ventricular septal defect with pulmonary stenosis or atresia, dextraposition of aorta,
and hypertrophy of right ventricle; ventricular septal defect with obstructed right ventricular outflow.; Fallot complex;
ICD-11 acronym : TOF;
ICD-11 inclusion : ventricular hypertrophy in tetralogy of Fallot; ventricular septal defect in tetralogy of Fallot; dextraposition of aorta in Fallot tetralogy; ventricular septal defect in Fallot tetralogy; pulmonary stenosis in tetralogy of Fallot; tetralogy of Fallot with pulmonary stenosis; interventricular septal defect with dextroposition of aorta, pulmonary stenosis and
hypertrophy of right ventricle; interventricular septal defect, in tetralogy of Fallot;
ICD-11 "other" category code : LA88.2Y;
ICD-11 "unspecified" category code : LA88.2Z;
Origin ID : 90973426;
UMLS CUI : C0039685;
Currated CISMeF NLP mapping
- ICD-10 Mapping
- Semantic type(s)
- UMLS correspondences (same concept)
A group of malformations with biventricular atrioventricular alignments or connections
characterized by anterosuperior deviation of the conal or outlet septum or its fibrous
remnant, narrowing or atresia of the pulmonary outflow, a ventricular septal defect
of the malalignment type, and biventricular origin of the aorta. Tetralogy of Fallot
will always have a ventricular septal defect, narrowing or atresia of the pulmonary
outflow, aortic override, and most often right ventricular hypertrophy.
