Mixed connective tissue disease

ICD-11 code : 4A43.3;

Preferred Label : Mixed connective tissue disease;

ICD-11 definition : Mixed connective tissue disease is an overlapping syndrome combining features of systemic lupus erythematosus, systemic sclerosis, and polymyositis with the presence of autoantibodies to U1-ribonucleoprotein. Raynaud's phenomenon is seen in nearly all patients and pulmonary arterial hypertension is the most common cause of death in MCTD patients.;

ICD-11 synonym : MCTD - [mixed connective tissue disease]; Sharp syndrome;

ICD-11 acronym : MCTD;

Details

Origin ID

891652224;

Automatic exact mappings (from CISMeF team)
- MCTD [MedDRA LLT]
- Other overlap syndromes [ICD-10 Sub-category]
- connective tissue disorders [MedlinePlus Topic]
- mixed connective tissue disease [DO Concept]
Currated CISMeF NLP mapping
- Eosinophilia myalgia syndrome [ICD-9 code]
- Mixed Connective Tissue Disease [NCIt concept]
- Mixed collagen vascular disease (disorder) [SNOMED CT concept]
- Mixed connective tissue disease [ORDO Disease]
- Mixed connective tissue disease [PASCAL descriptor]
- Mixed connective tissue disease [MedDRA Preferred Term]
- Sharp's syndrome [MedDRA LLT]
- mixed connective tissue disease [MeSH Descriptor]
- mixed connective tissue disease [MeSH concept]
ICD-10 Mapping
- Other overlap syndromes [ICD-10 Sub-category]

Keyword's position in hierarchy(ies) :

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