" /> Paroxysmal nocturnal haemoglobinuria - CISMeF





ICD-11 code : 3A21.0;

Preferred Label : Paroxysmal nocturnal haemoglobinuria;

ICD-11 definition : Paroxysmal nocturnal hemoglobinuria (PNH) is an acquired clonal hematopoietic stem cell disorder characterized by corpuscular hemolytic anemia, bone marrow failure and frequent thrombotic events.;

ICD-11 synonym : Marchiafava-Micheli disease; Marchiafava-Micheli syndrome;

ICD-11 inclusion : nocturnal paroxysmal haematuria; nocturnal haemoglobinuria; nocturnal paroxysmal haemoglobinaemia;

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Paroxysmal nocturnal hemoglobinuria (PNH) is an acquired clonal hematopoietic stem cell disorder characterized by corpuscular hemolytic anemia, bone marrow failure and frequent thrombotic events.

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27/07/2025


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