Paroxysmal nocturnal haemoglobinuria

ICD-11 code : 3A21.0;

Preferred Label : Paroxysmal nocturnal haemoglobinuria;

ICD-11 definition : Paroxysmal nocturnal hemoglobinuria (PNH) is an acquired clonal hematopoietic stem cell disorder characterized by corpuscular hemolytic anemia, bone marrow failure and frequent thrombotic events.;

ICD-11 synonym : Marchiafava-Micheli disease; Marchiafava-Micheli syndrome;

ICD-11 inclusion : nocturnal paroxysmal haematuria; nocturnal haemoglobinuria; nocturnal paroxysmal haemoglobinaemia;

Details

Origin ID

859588467;

Currated CISMeF NLP mapping
- Nocturnal paroxystic anemia [PASCAL descriptor]
- Paroxysmal Nocturnal Hemoglobinuria [NCIt concept]
- Paroxysmal nocturnal haemoglobinuria [MedDRA Preferred Term]
- Paroxysmal nocturnal haemoglobinuria [Marchiafava-Micheli] [ICD-10 Sub-category (who)]
- Paroxysmal nocturnal hemoglobinuria [ORDO Disease]
- Paroxysmal nocturnal hemoglobinuria [HPO term]
- Paroxysmal nocturnal hemoglobinuria [MedDRA LLT]
- Paroxysmal nocturnal hemoglobinuria (disorder) [SNOMED CT concept]
- Paroxysmal nocturnal hemoglobinuria 1 [OMIM Phenotype]
- nocturnal paroxysmal hemoglobinuria [Blood Transfusion thesaurus concept]
- paroxysmal nocturnal hemoglobinuria [MeSH concept]
- paroxysmal nocturnal hemoglobinuria [SNOMED Notion]
- paroxysmal nocturnal hemoglobinuria [Disease (Nov.)]
- paroxysmal nocturnal hemoglobinuria [DO Concept]
ICD-10 Mapping
- Paroxysmal nocturnal hemoglobinuria [Marchiafava-Micheli] [ICD-10 Sub-category]
Validated automatic mappings to NTBT
- hemoglobinuria, paroxysmal [MeSH Descriptor]

Keyword's position in hierarchy(ies) :

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