ICD-11 code : 4A41.0;
Preferred Label : Dermatomyositis;
ICD-11 definition : Dermatomyositis is an inflammatory myopathy, showing progressive, symmetrical muscle
weakness, low muscle endurance, and cutaneous manifestations such as Gottron's papules,
heliotrope rash, shawl sign, V-sign and mechanic's hand. Internal organ manifestations
such as interstitial pneumonia (pneumonitis) and myocarditis sometimes develop. The
skin rash may precede the muscle symptoms and may be the only clinical sign of dermatomyositis
in some patients (clinically, amyopathic dermatomyositis).;
ICD-11 inclusion : Petges-Clejat syndrome;
ICD-11 "unspecified" category code : 4A41.0Z;
Origin ID : 739030149;
UMLS CUI : C0011633;
Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
- ICD-10 Mapping
- See also inter- (CISMeF)
- Semantic type(s)
- UMLS correspondences (same concept)
- Validated automatic mappings to NTBT
Dermatomyositis is an inflammatory myopathy, showing progressive, symmetrical muscle
weakness, low muscle endurance, and cutaneous manifestations such as Gottron's papules,
heliotrope rash, shawl sign, V-sign and mechanic's hand. Internal organ manifestations
such as interstitial pneumonia (pneumonitis) and myocarditis sometimes develop. The
skin rash may precede the muscle symptoms and may be the only clinical sign of dermatomyositis
in some patients (clinically, amyopathic dermatomyositis).
