ICD-11 code : 3A20.3;
Preferred Label : Paroxysmal cold haemoglobinuria;
ICD-11 definition : Paroxysmal cold hemoglobinuria is a very rare subtype of autoimmune hemolytic anemia
(AIHA), caused by the presence of cold-reacting autoantibodies in the blood and characterized
by the sudden presence of hemoglobinuria, typically after exposure to cold temperatures.
PCH is thought to account for at most 2-10% of cases of AIHA.;
ICD-11 synonym : Donath-Landsteiner syndrome;
Origin ID : 715111132;
Automatic exact mappings (from CISMeF team)
- ICD-10 Mapping
Paroxysmal cold hemoglobinuria is a very rare subtype of autoimmune hemolytic anemia
(AIHA), caused by the presence of cold-reacting autoantibodies in the blood and characterized
by the sudden presence of hemoglobinuria, typically after exposure to cold temperatures.
PCH is thought to account for at most 2-10% of cases of AIHA.
