Primary effusion lymphoma

ICD-11 code : 2A81.9;

Preferred Label : Primary effusion lymphoma;

ICD-11 definition : An aggressive non-Hodgkin B-cell lymphoma composed of large cells, presenting as a serous effusion without detectable tumor masses. It is universally associated with human herpes virus 8 (HHV-8)/Kaposi sarcoma herpes virus (KSHV) [HHV-8/KSHV]. It mostly occurs in the setting of immunodeficiency; most cases have been reported in HIV positive patients. The most common sites of involvement are the pleural, pericardial, and peritoneal cavities. The prognosis is extremely unfavorable.;

Details

Origin ID

697911710;

Currated CISMeF NLP mapping
- PEL (body structure) [SNOMED CT concept]
- Primary Effusion Lymphoma [NCIt concept]
- Primary effusion lymphoma [ICD-O code]
- Primary effusion lymphoma [MedDRA Preferred Term]
- Primary effusion lymphoma [PASCAL descriptor]
- Primary effusion lymphoma [ORDO Disease]
- Primary effusion lymphoma (disorder) [SNOMED CT concept]
- Primary effusion lymphoma (morphologic abnormality) [SNOMED CT concept]
- lymphoma, primary effusion [MeSH Descriptor]
- lymphoma, primary effusion [MeSH concept]
ICD-10 Mapping
- Diffuse large B-cell lymphoma [ICD-10 Sub-category]

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