ICD-11 code : 8C71.4;
Preferred Label : Neuromyotonia;
ICD-11 definition : Neuromyotonia or Isaac's syndrome is an immune-mediated peripheral nerve disorder
characterized by continuous muscle fiber activity at rest resulting in muscle stiffness,
cramps, myokymia, and pseudomyotonia.;
ICD-11 synonym : Isaacs neuromyotonia;
ICD-11 inclusion : Isaacs-Mertens syndrome; Isaacs syndrome;
Origin ID : 646523932;
Automatic exact mappings (from CISMeF team)
ICD-10 Mapping
Neuromyotonia or Isaac's syndrome is an immune-mediated peripheral nerve disorder
characterized by continuous muscle fiber activity at rest resulting in muscle stiffness,
cramps, myokymia, and pseudomyotonia.