Retinal vasculopathy and cerebral leukodystrophy

ICD-11 code : 9B78.0;

Preferred Label : Retinal vasculopathy and cerebral leukodystrophy;

ICD-11 definition : Retinal vasculopathy and cerebral leukodystrophy is an inherited group of small vessel diseases comprised of cerebroretinal vasculopathy, hereditary vascular retinopathy and hereditary endotheliopathy with retinopathy, nephropathy and stroke (HERNS); all exhibiting progressive visual impairment as well as variable cerebral dysfunction.;

Details

Origin ID

554838792;

Automatic exact mappings (from CISMeF team)
- Retinal vasculopathy with cerebral leukoencephalopathy and systemic manifestations [ORDO Disease]
- Vasculopathy, retinal, with cerebral leukoencephalopathy and systemic manifestations [OMIM Phenotype]
- retinal vasculopathy with cerebral leukodystrophy [DO Concept]
- vasculopathy, retinal, with cerebral leukodystrophy [MeSH Supplementary Concept]
- vasculopathy, retinal, with cerebral leukodystrophy [MeSH concept]
ICD-10 Mapping
- Other retinal disorders [ICD-10 category]

Keyword's position in hierarchy(ies) :

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