ICD-11 code : 8E01.1;
Preferred Label : Kuru;
ICD-11 definition : A disease of the nervous system, caused by a prion. This disease is characterized
by limb pain, ataxia, tremors, decreased coordination, or emotional changes, and is
fatal. Transmission is by ingestion of infected human brain, or direct contact. Confirmation
is commonly by clinical signs, or pathological examination of the brain.;
ICD-11 synonym : kuru encephalitis; kuru disease;
Origin ID : 553889510;
Automatic exact mappings (from CISMeF team)
- Kuru [MedDRA Preferred Term]
ICD-10 Mapping
A disease of the nervous system, caused by a prion. This disease is characterized
by limb pain, ataxia, tremors, decreased coordination, or emotional changes, and is
fatal. Transmission is by ingestion of infected human brain, or direct contact. Confirmation
is commonly by clinical signs, or pathological examination of the brain.