ICD-11 code : BC65.2;
Preferred Label : Short QT syndrome;
ICD-11 definition : Familial short QT syndrome is a rare cardiac rhythm disorder that associates a short
QT interval (QT and QTc 300 ms) on the surface electrocardiogram (ECG) with a high
risk of syncope or sudden death due to malignant ventricular arrhythmia.;
ICD-11 synonym : Familial short QT syndrome;
Origin ID : 553392015;
Automatic exact mappings (from CISMeF team)
ICD-10 Mapping
Familial short QT syndrome is a rare cardiac rhythm disorder that associates a short
QT interval (QT and QTc 300 ms) on the surface electrocardiogram (ECG) with a high
risk of syncope or sudden death due to malignant ventricular arrhythmia.