ICD-11 code : 3B14.2;
Preferred Label : Combined deficiency of vitamin K-dependent clotting factors;
ICD-11 definition : Hereditary combined vitamin K-dependent clotting factors deficiency (VKCFD) is a congenital
bleeding disorder resulting from variably decreased levels of coagulation factors
II, VII, IX and X, as well as natural anticoagulants protein C, protein S and protein
Z.;
ICD-11 synonym : Combined deficiency of factors II,VII,IX and X; Vitamin K epoxide reductase deficiency;
Origin ID : 54644599;
Automatic exact mappings (from CISMeF team)
ICD-10 Mapping
Hereditary combined vitamin K-dependent clotting factors deficiency (VKCFD) is a congenital
bleeding disorder resulting from variably decreased levels of coagulation factors
II, VII, IX and X, as well as natural anticoagulants protein C, protein S and protein
Z.