ICD-11 code : 8B61.3;
Preferred Label : Adult onset spinal muscular atrophy, Type IV;
ICD-11 definition : In SMA type 4 weakness, most commonly develops after 35 years of age (less commonly
between 18 to 35 years old). Weakness of proximal muscles is more prominent in the
legs than in the arms. Insidious onset and very slow progression are the characteristic
features, and life span is normal.;
Origin ID : 443229384;
Automatic exact mappings (from CISMeF team)
- ICD-10 Mapping
In SMA type 4 weakness, most commonly develops after 35 years of age (less commonly
between 18 to 35 years old). Weakness of proximal muscles is more prominent in the
legs than in the arms. Insidious onset and very slow progression are the characteristic
features, and life span is normal.
