ICD-11 code : LB13.0;
Preferred Label : Congenital hypertrophic pyloric stenosis;
ICD-11 definition : A not uncommon congenital malformation of the stomach of unknown cause in which there
is hypertrophy and hyperplasia of the circular muscle of the pylorus. Symptoms of
gastric outlet obstruction usually appear between the third and sixth weeks of life.
The anomaly is manifested by intermittent vomiting (which increases in frequency and
becomes projectile), regurgitation, weight loss, dehydration, electrolyte imbalance,
sometimes a small palpable pyloric mass, and visible peristaltic contractions across
the epigastrium; there may also be jaundice. Some cases appear to be familial (possibly
of autosomal dominant inheritance).;
ICD-11 synonym : congenital hypertrophy of the pylorus; Congenital or infantile constriction of pylorus; congenital constriction of the pylorus; infantile pyloric obstruction; achalasia of the pylorus; infantile stenosis of the pylorus; infantile stricture of the pylorus; infantile hypertrophy of the pylorus; infantile constriction of the pylorus; infantile pyloric hypertrophy; infantile hypertrophic pyloric stenosis; congenital stricture of the pylorus; congenital stenosis of the pylorus;
ICD-11 inclusion : Congenital or infantile spasm of pylorus; pyloric constriction; congenital pyloric stenosis; infantile pyloric stricture; infantile pyloric stenosis; congenital pylorospasm; congenital pyloric spasm; congenital pyloric stricture; congenital or infantile obstruction of pylorus; pylorus achalasia; congenital spasm of pylorus;
Origin ID : 224753192;
UMLS CUI : C0700639;
Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
- ICD-10 Mapping
- Semantic type(s)
- UMLS correspondences (same concept)
A not uncommon congenital malformation of the stomach of unknown cause in which there
is hypertrophy and hyperplasia of the circular muscle of the pylorus. Symptoms of
gastric outlet obstruction usually appear between the third and sixth weeks of life.
The anomaly is manifested by intermittent vomiting (which increases in frequency and
becomes projectile), regurgitation, weight loss, dehydration, electrolyte imbalance,
sometimes a small palpable pyloric mass, and visible peristaltic contractions across
the epigastrium; there may also be jaundice. Some cases appear to be familial (possibly
of autosomal dominant inheritance).
