ICD-11 code : 2B56.1;
Preferred Label : Angiosarcoma of skin;
ICD-11 definition : A malignant tumour arising from the endothelial cells of the blood vessels. Microscopically,
it is characterised by frequently open vascular anastomosing and branching channels.
The malignant cells that line the vascular channels are spindle or epithelioid and
often display hyperchromatic nuclei. Angiosarcomas most frequently occur in the skin
and breast. Patients with long-standing lymphoedema are at increased risk of developing
angiosarcoma.;
ICD-11 synonym : Malignant haemangioendothelioma of skin; Cutaneous angiosarcoma; Haemangiosarcoma of skin; Lymphangiosarcoma of skin;
ICD-11 inclusion : Epithelioid haemangioendothelioma of skin; Retiform haemangioendothelioma of skin;
Origin ID : 2111451719;
Automatic exact mappings (from CISMeF team)
A malignant tumour arising from the endothelial cells of the blood vessels. Microscopically,
it is characterised by frequently open vascular anastomosing and branching channels.
The malignant cells that line the vascular channels are spindle or epithelioid and
often display hyperchromatic nuclei. Angiosarcomas most frequently occur in the skin
and breast. Patients with long-standing lymphoedema are at increased risk of developing
angiosarcoma.
