Congenital pulmonary airway malformations

ICD-11 code : LA75.4;

Preferred Label : Congenital pulmonary airway malformations;

ICD-11 definition : A disease caused by failure of the bronchial structure to correctly develop during the antenatal period. This disease may present with severe respiratory distress in the newborn period, acute respiratory distress or infection later in life, or may be asymptomatic. This disease can be distinguished from other lesions and normal lung by polypoid projections of the mucosa, an increase in smooth muscle and elastic tissue within the cyst walls, an absence of cartilage in the cystic parenchyma, mucous secreting cells, and the absence of inflammation.;

ICD-11 synonym : Congenital cystic adenomatoid malformation; Congenital lung cyst; Congenital cystic disease of lung; CCAM - [Congenital cystic adenomatoid malformation]; Congenital cystic lung;

ICD-11 acronym : CCAM;

ICD-11 inclusion : Congenital polycystic lung; Congenital honeycomb lung; Congenital polycystic disease of lung; Multiple congenital bronchogenic cysts;

Details

Origin ID

2091138945;

UMLS CUI

C0158641;

Automatic exact mappings (from CISMeF team)
- Congenital cystic adenomatoid malformation of lung (disorder) [SNOMED CT concept]
- Congenital cystic lung [ICD-9 code]
- Congenital cystic lung [ICD-10 Sub-category]
- Congenital pulmonary airway malformation [ORDO Disease]
- Congenital pulmonary airway malformation [HPO term]
- common classification of medical procedures [Artificial nutrition thesaurus concept]
- cystic adenomatoid malformation of lung, congenital [MeSH Descriptor]
- healthcare common procedure coding system [MeSH Descriptor]
Currated CISMeF NLP mapping
- Congenital cystic lung [MedDRA Preferred Term]
- Congenital cystic lung (disorder) [SNOMED CT concept]
- Cystic lung, congenital [MedDRA LLT]
- congenital cystic lung [SNOMED Notion]
ICD-10 Mapping
- Congenital cystic lung [ICD-10 Sub-category]
Semantic type(s)
- Congenital Abnormality [UMLS semantic type]
UMLS correspondences (same concept)
- Congenital cystic lung [ICD-9 code]
- Congenital cystic lung [ICD-10 Sub-category]
- Congenital cystic lung [MedDRA Preferred Term]
- Congenital cystic lung [MedDRA LLT]
- Congenital cystic lung (disorder) [SNOMED CT concept]
- Cystic lung, congenital [MedDRA LLT]
- congenital cystic lung [SNOMED Notion]
Validated automatic mappings to BTNT
- Congenital cystic lung [ICD-10 Sub-category (who)]

Keyword's position in hierarchy(ies) :

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